Differential diagnosis of bell-shaped (small) chest in neonates
Approach to the differential diagnosis of a bell-shaped (small) chest in neonates: Oligohydramnios – due to pulmonary hypoplasia. Respiratory distress syndrome – due to pulmonary hypoexpansion. Neuromuscular paralysis – due to hypotonia causing body wall edema.
Asphyxiating thoracic dysplasia | Radiology Reference Article ...
2023年5月18日 — Asphyxiating thoracic dysplasia, also known as Jeune syndrome, is a type of rare short limb skeletal dysplasia, which is primarily characterized by a constricted long narrow thoracic cavity, cystic renal dysplasia and characteristic skeletal features.
Asphyxiating Thoracic Dystrophy - Symptoms, Causes, Treatment
2020年12月3日 — Asphyxiating thoracic dystrophy (ATD) is a very rare form of skeletal dysplasia that primarily affects development of the bone structure of the chest (thorax) resulting in a very narrow and bell-shaped chest.
Respiratory distress syndrome | Radiology Reference Article ...
2024年8月22日 — bell-shaped thorax. air bronchograms may be evident. Hyperinflation makes the diagnosis less likely, unless the patient is intubated. If treated with surfactant therapy, there may be an asymmetric improvement as more surfactant may reach certain parts of the lungs than others. Ultrasound
Jeune syndrome - Children's Hospital of Philadelphia
Also called asphyxiating thoracic dystrophy. Children born with Jeune syndrome have a small chest and ribcage. The child may have life-threatening breathing problems because there isn’t enough room in the chest for the lungs to develop properly or to expand fully during breathing.
Jeune's Syndrome - Nationwide Children's Hospital
The chest cage is extremely small and doesn't have enough room for proper breathing. The ribs are broad, short and irregularly joined between the cartilage and sternum, or breastbone. This produces a bell-shaped, inflexible chest cavity, which doesn't grow well in time.
Jeune syndrome (asphyxiating thoracic dystrophy - ATD)
Children with Jeune syndrome, also known as asphyxiating thoracic dystrophy (ATD), experience abnormalities in the shape of their bones throughout their body. Because of their short ribs and narrow chest, children with Jeune syndrome have a bell-shaped chest that affects their breathing.
Asphyxiating thoracic dystrophy - MedlinePlus
Asphyxiating thoracic dystrophy, also known as Jeune syndrome, is an inherited disorder of bone growth characterized by a narrow chest, short ribs, shortened bones in the arms and legs, short stature, and extra fingers and toes (polydactyly).
Infant respiratory distress syndrome - Wikipedia
The diagnosis is made by the clinical picture and the chest X-ray, which demonstrates decreased lung volumes (bell-shaped chest), absence of the thymus (after about six hours), a small (0.5–1 mm), discrete, uniform infiltrate (sometimes described as a "ground glass" appearance or "diffuse airspace and interstitial opacities") that involves ...
What You Should Know About Jeune Syndrome - Verywell Health
2024年5月6日 — Jeune syndrome, also known as asphyxiating thoracic dystrophy, is an inherited form of dwarfism. It causes the chest wall to be very small. This makes breathing difficult and can be life-threatening. The survival rate for Jeune syndrome greatly increases with surgery.