ocular involvement occurs in up to 60% of WG/GPA patients and not infrequently forms the initial presentation of the disease. [4] Granulomatosis with polyangiitis (previously known as Wegener's ...

Children with AAV and kidney disease face increased risks for long-term renal damage at 1 year, despite the majority achieving inactive renal disease by this time.

Wegener's granulomatosis/granulomatosis with polyangiitis is a fatal disease if left untreated, and the natural history is for only 50% of patients to survive 5 ...